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Dandy-Walker Malformation: Analysis of 19 Cases
George A. Alexiou, MD, PhD*,
George Sfakianos, MD, PhD,
and
Neofytos Prodromou, MD, PhD
Department of Neurosurgery, Children’s Hospital ‘‘Agia Sofia,’’ Athens, Greece
* To whom correspondence should be addressed. E-mail: alexiougrg{at}yahoo.gr.
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Abstract |
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Dandy-Walker malformation is a congenital disorder that involves the cerebellum and fourth ventricle. Regarding treatment, there is still controversy over the optimum surgical management. In the current study, we present 19 consecutive cases of Dandy-Walker malformation diagnosed between January 1992 and January 2008 that were treated in our institute. All patients presented with hydrocephalus at the time of diagnosis and were treated surgically. Combined drainage of the ventricular system and posterior fossa cyst, using a 3-way connector was performed in 5 patients. Posterior fossa cyst drainage alone was performed in 10 patients and the remaining 4 patients were treated by ventricular drainage alone. All patients improved after treatment. Dandy-Walker malformation is a developmental abnormality of the central nervous system associated with various brain and extracranial abnormalities. Surgical treatment remains controversial, whereas prognosis varies greatly according to the severity of syndrome and associated comorbidities.
First published on October 15, 2009
Journal of Child Neurology 2009, doi:10.1177/0883073809338410
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