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Rapidly Declining Unilateral Hearing Within 1 Month in a Newborn With Internal Auditory Canal Stenosis and Facial Palsy

¹ Department of Pediatrics, Chung Shan Medical University Hospital, and Institute of Medicine, School of Medicine, Chung Shan Medical University, Taichung, Taiwan
² Institute of Medicine, School of Medicine, Chung Shan Medical University, and Dept of Otolaryngology, Chung Shan Medical University Hospital, Taichung, Taiwan
³ Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
⁴ Institute of Medicine, School of Medicine, Chung Shan Medical University, Taichung, Taiwan

^* To whom correspondence should be addressed. E-mail: y610{at}mercury.csmu.edu.tw.

	Abstract

Most newborns with congenital unilateral facial palsy are expected to recover; however, when a patient has hearing loss, underlying developmental ear structure abnormalities should be investigated, particularly when the patient has internal auditory canal stenosis, which is rarely reported in newborns. All cases of internal auditory canal stenosis are accompanied by concomitant unilateral or bilateral hearing loss, but none with progressive hearing loss has been reported. We present the case of a newborn with rapidly declining hearing in the left ear within 1 month after birth. The hearing decline was associated with unilateral facial palsy. Using high-resolution computed tomography (CT) of the temporal bone, we diagnosed the patient with congenital internal auditory canal stenosis. This is the first case detected with progressive hearing loss after birth, which implies that prompt diagnosis and early habilitation are warranted, even when the hearing loss is initially mild.

First published on September 17, 2009
Journal of Child Neurology 2009, doi:10.1177/0883073809340919


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