This Article Full Text (PDF) References Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Saved Citations Download to citation manager Request Permissions Request Reprints Add to My Marked Citations Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Citing Articles via Scopus Google Scholar Articles by Greco, F. Articles by Parano, E. Search for Related Content PubMed PubMed Citation Articles by Greco, F. Articles by Parano, E. Pubmed/NCBI databases Medline Plus Health Information CT Scans MRI Scans Social Bookmarking                         What's this?

Hemihydranencephaly: Case Report and Literature Review

Division of Pediatric Neurology, Department of Pediatrics University of Catania, Catania, Italy

Maria Finocchiaro, MD

Division of Pediatric Neurology, Department of Pediatrics University of Catania, Catania, Italy

Piero Pavone, MD

Division of Pediatric Neurology, Department of Pediatrics University of Catania, Catania, Italy

Rosario R. Trifiletti, MD

Department of Neurology, Neuroscience and Pediatrics, The New York Hospital-Cornell, University Medical Center New York, New York

Enrico Parano, MD, IBFSNC

The National Research Council of Italy-CNR Catania, Italy

Hydranencephaly is a severe brain condition characterized by complete or almost complete absence of cerebral cortex with preservation of meninges, basal ganglia, pons, medulla, cerebellum, and falx. It has been ascribed to different causes (infections, irradiations, fetal anoxia, medications, twin-twin transfusion), all leading to vascular disruption. Hemihydranencephaly is an extremely rare condition in which the vascular anomaly is unilateral. We report on a patient who was suspected to have hydrocephalus in utero; a brain magnetic resonance imaging scan showed left-sided hydranencephaly with preservation of basal ganglia. The patient developed signs of right hemiparesis but notably has only mild language delay. The available literature on hemihydranencephaly is reviewed. (J Child Neurol 2001;16:218-221).

Journal of Child Neurology, Vol. 16, No. 3, 218-221 (2001)
DOI: 10.1177/088307380101600311


CiteULike    Complore    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter    What's this?

This article has been cited by other articles:

				E. L. Altschuler, B. Matsumura, J. Capoor, K. Weinshelbaum, and H. Ghuznavi Left-Hemispheric Hydranencephaly With Less Favorable Findings Pediatrics, December 1, 2005; 116(6): 1603 - 1604. [Full Text] [PDF]

				S. Ulmer and O. Jansen Left-Hemispheric Hydranencephaly With Less Favorable Findings: In Reply Pediatrics, December 1, 2005; 116(6): 1604 - 1604. [Full Text] [PDF]

				S. Ulmer, F. Moeller, M. A. Brockmann, J. P. Kuhtz-Buschbeck, U. Stephani, and O. Jansen Living a Normal Life With the Nondominant Hemisphere: Magnetic Resonance Imaging Findings and Clinical Outcome for a Patient With Left-Hemispheric Hydranencephaly Pediatrics, July 1, 2005; 116(1): 242 - 245. [Abstract] [Full Text] [PDF]

				C. A. McKnight, T. L. Reynolds, M. Haulena, A. deLahunta, and F. M. D. Gulland Congenital Hemicerebral Anomaly in a Stranded Pacific Harbor Seal (Phoca vitulina richardsi) J. Wildl. Dis., July 1, 2005; 41(3): 654 - 658. [Abstract] [Full Text] [PDF]