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Juvenile Dermatomyositis Presenting With AnasarcaDepartment of Pediatrics, Division of Pediatric Neurology, Baskent University Faculty of Medicine, Ankara, Turkey, semra_saygi{at}yahoo.com
Department of Pediatrics, Division of Pediatric Neurology, Baskent University Faculty of Medicine, Ankara, Turkey
Department of Pediatrics, Division of Child Nephrology and Rheumatology, Baskent University Faculty of Medicine, Ankara, Turkey
Department of Pediatrics, Division of Child Nephrology and Rheumatology, Baskent University Faculty of Medicine, Ankara, Turkey
Department of Radiology, Baskent University Faculty of Medicine, Ankara, Turkey
Department of Pediatrics, Division of Child Hematology, Baskent University Faculty of Medicine, Ankara, Turkey Generalized edema can occur during the course of juvenile dermatomyositis. In this article, a 4-year-old boy with generalized nonpitting edema and proximal weakness is reported. Characteristic cutaneous lesions, laboratory tests, results of electromyography, and magnetic resonance imaging findings resulted in a diagnosis of juvenile dermatomyositis. He was treated with corticosteroids and methotrexate. It is concluded that the generalized edema may appear as the presenting cutaneous manifestation of juvenile dermatomyositis.
Key Words: juvenile dermatomyositis anasarca
Journal of Child Neurology, Vol. 23, No. 11,
1353-1356 (2008) |
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